A Case Report On Prune Belly Syndrome

Pharmaceutical Science-Pharmacy Practice

Authors

  • Dr. Clince Junior Resident, Department of Paediatrics, Sree Balaji Medical College and Hospital, Chennai, Tamil Nadu, India https://orcid.org/0000-0002-0736-2309
  • Dr.Ravanagomagan M.G Assistant Professor, Department of Paediatrics, Sree Balaji Medical College and Hospital, Chennai, Tamil Nadu, India
  • Dr.Shanthi Ramesh Professor, Department of Paediatrics, Sree Balaji Medical College and Hospital, Chennai, Tamil Nadu, India
  • Dr.Sundari .S HOD and Professor, Department of Paediatrics, Sree Balaji Medical College and Hospital. Chennai, Tamil Nadu, India

DOI:

https://doi.org/10.22376/ijpbs/lpr.2022.12.5.L178-181

Keywords:

Hydronephrosis, Big Ureter, Undescended Testis, Prune Belly Syndrome

Abstract

Eagle-Barrett syndrome’ is the other name for prune belly syndrome. The classical triad of urinary tract anomalies,
deficient abdominal musculature, and bilateral cryptorchidism. It is a congenital anomaly of unknown aetiology, most commonly
seen in males. It is seen in one and 30,000 live births.96% of them are males. In this case report, we present a boy child born to
A 38-year-old multigravida mother with a previous history of three vaginal deliveries. On examination of the baby, the following
features are to be found-hypotonia, deficiency of abdominal muscle, undescended testis, a palpable bladder and kidney. Radiological
imaging showed gross hydronephrosis on both sides and big ureter. The baby was diagnosed with Prune Belly syndrome.
Ultrasound investigations done during the antenatal period, helps in directing anomalies of the kidney which is to be followed in
the postnatal period. The aim of the writing this case report is to establish the importance of antenatal diagnosis of congenital
malformations including Eagle-Barrett Syndrome among many others. Prenatal diagnosis of PBS should be considered whenever
the following ultra- sound anomalies are clearly identified: oligohydramnios, urinary abnormalities (dilatation of the urinary tract,
megacystis, bilateral hydroureteronephrosis), and the absence of abdominal musculature. Routine screening during the antenatal
period with ultrasound helps in detecting anomalies of the kidney at an earlier stage . This help in initiating optimal treatment to
avoid the fatal cause of Prune Belly Syndrome

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Published

2022-08-17

How to Cite

Clince, D. ., M.G, D., Ramesh, D., & .S, D. (2022). A Case Report On Prune Belly Syndrome: Pharmaceutical Science-Pharmacy Practice. International Journal of Life Science and Pharma Research, 12(5), L178-P181. https://doi.org/10.22376/ijpbs/lpr.2022.12.5.L178-181

Issue

Section

Case Study